Clinical and Radiographic Features of Nevoid Basal Cell Carcinoma Syndrome: A Case Report

Authors

G Subhas Babu, Department of Oral Medicine and Radiology, A B Shetty Memorial Institute of Dental Sciences, Mangaluru, IndiaFollow
Devika S. Pillai, Department of Oral Medicine and Radiology, Saveetha Institute of Medical and Technical Sciences, Chennai, IndiaFollow
Shruthi Hegde, Department of Oral Medicine and Radiology, A B Shetty Memorial Institute of Dental Sciences, Mangaluru, India
Padmaraj Hegde, Department of Oral and Maxillofacial Surgery, A B Shetty Memorial Institute of Dental Sciences, Mangaluru, India
Vidya Ajila, Department of Oral Medicine and Radiology, A B Shetty Memorial Institute of Dental Sciences, Mangaluru, India

Abstract

Nevoid Basal Cell Carcinoma Syndrome, also called as Gorlin Gotz syndrome is an autosomal dominant disorder characterized by the presence of multiple odontogenic keratocysts (OKCs) of the jaw, basal cell carcinomas and skeletal anomalies. Presence of multiple OKCs is the first clinical manifestation in majority of the cases. Early diagnosis and treatment are of utmost importance in reducing the severity of this syndrome. We hereby report a rare case of Gorlin Goltz syndrome in a 28 years old female patient who presented with multiple cystic lesions in the jaws. Present case also highlights the clinical, radiographic and histopathologic features of this uncommon syndrome.

References

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Recommended Citation

Babu, G., Pillai, D. S., Hegde, S., Hegde, P., & Ajila, V. Clinical and Radiographic Features of Nevoid Basal Cell Carcinoma Syndrome: A Case Report. J Dent Indones. 2022;29(3): 224-227